Langerhans cell histiocytosis: a rare cause of cholestasis in adult patients. Case report. Histiocitosis de Langerhans: causa infrecuente de colestasis en el. a Unidad Médico-Quirúrgica de Enfermedades Respiratorias. Área de Neumopatías Intersticiales y Ocupacionales. Hospital Universitario Virgen del Rocío. Abstract. GOMEZ, ANA MARÍA et al. Langerhans cell histiocytosis in children. A description of 10 cases. CES Med. [online]. , vol, n.2, pp

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Determinants of survival in pulmonary Langerhans’ cell granulomatosis histiocytosis X. Translators working for the Journal are in charge of the corresponding translations. CiteScore measures average citations received per document published. Previous article Next article.

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Etxezarraga 2 and M. It was decided to perform a bypass surgery and a hepaticojejunostomy and a gastrojejunostomy were performed. How to cite this article. The Spanish Association of Pediatrics has as one of its main objectives the dissemination of rigorous and updated scientific information on the histioxitosis areas of pediatrics.

Three histological patterns have been described: Dina J, et al. Langerhans cell histiocytosis in children.

Are you a health professional able to prescribe or dispense drugs? The goal with the description of this cases series is to highlight the importance and awareness to a timely diagnosis and management of bistiocitosis entity, for a better quality of life and longer survival.


Of the 10 patients 5 had risk organ involvement and 1 died in the observation period.

Histiocitosis de células de Langerhans en niños. Descripción de 10 casos

To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior. One year before coming to our hospital for the first time, he had presented an episode of acute pancreatitis with pseudocyst formation.

Histiocytosis; Langerhans cells; Pediatrics. To improve our histiocirosis and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of re customer behavior.

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Services on Demand Article. Liver involvement langdrhans Langehan’s cell histiocytosis. Ann Thoracic Surg, 30pp. From Monday langerhasn Friday from 9 a. All manuscripts are sent to peer-review and handled by the Editor or an Associate Editor from the team. The pathological diagnosis was chronic pancreatitis. A biopsy of the lesions showed that these lesions were compatible with Langerhans cell histiocytosis.

Subscribe to our Newsletter. Liver involvement in Langerhans’ cell histiocytosis: Discussion There are two patterns of involvement: You can change the settings or obtain more information by clicking here. Bravo 1M. The Impact Factor measures the average number of citations received in a particular year by papers published in the journal during the two receding years.

Subscribe to our Newsletter. Annals of Pediatrics is the Body of Scientific Expression of the Association and is the vehicle through which members communicate.


It was informed a cholestasis due to long term obstruction of large biliary ducts. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. Pemphigus Vegetans in the Inguinal Folds. Eur Respir J, 9pp. Dear Editor, We present a 42 year old man, with a history of central diabetes insipidus since childhood, primary hyperthyroidism with negative antibodies and seizures since early adulthood.

Gastrointestinal involvement in Langerhans cell histiocytosis. Journal of Hepatology ; Langerhans cell histiocytosis was confirmed in both cases with S immunohistochemical staining. However, if risk organs are involved, other chemotherapeutics are needed as well 6-mercaptopurine and metotrexate. Langerhans cell histiocytosis infiltration into pancreas and kidney. Open biopsy for chronic diffuse infiltration lung disease: Liver transplantation in an adult with sclerosing cholangitis due to Langerhans cell histiocytosis.

The disease prognosis and its response to treatment lngerhans better in the single system form, particularly with bone involvement, and much worse in the multi-system form, especially if several risk organs are involved liver, spleen, bone marrow and lung.